enzymology, a 1-pyrroline-5-carboxylate dehydrogenase (EC 1.2.1.88) is an enzyme that catalyzes the chemical reaction (S)-1-pyrroline-5-carboxylate + NAD+ +...
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degradation, the enzyme proline dehydrogenase produces P5C from proline, and the enzyme 1-pyrroline-5-carboxylate dehydrogenase converts GSA to glutamate....
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Hyperprolinemia (redirect from Pyrroline-5-carboxylate dehydrogenase deficiency)
broken down properly by the enzymes proline oxidase or pyrroline-5-carboxylate dehydrogenase, causing a buildup of proline in the body. Mutations in...
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Delta-1-pyrroline-5-carboxylate dehydrogenase, mitochondrial is an enzyme that in humans is encoded by the ALDH4A1 gene. This protein belongs to the aldehyde...
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tremens Delusional disorder Delleman–Oorthuys syndrome Delta-1-pyrroline-5-carboxylate dehydrogenase deficiency Delta-sarcoglycanopathy Dementia Dementia, alcohol...
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Delta-1-pyrroline-5-carboxylate synthetase (P5CS) is an enzyme that in humans is encoded by the ALDH18A1 gene. This gene is a member of the aldehyde dehydrogenase...
14 KB (1,678 words) - 15:44, 27 September 2023
(S)-1-pyrroline-5-carboxylate during proline catabolism. The end product of this reaction is then further oxidized in a (S)-1-pyrroline-5-carboxylate dehydrogenase...
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1-piperideine-2-carboxylate/1-pyrroline-2-carboxylate reductase (NADPH) EC 1.5.1.22: strombine dehydrogenase EC 1.5.1.23: tauropine dehydrogenase EC 1.5.1.24:...
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reaction D-proline + acceptor ⇌ {\displaystyle \rightleftharpoons } 1-pyrroline-2-carboxylate + reduced acceptor This enzyme is a flavoprotein (FAD). Tani Y...
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either spontaneously cyclize to form 1-pyrroline-5-carboxylic acid, which is reduced to proline by pyrroline-5-carboxylate reductase (using NADH or NADPH)...
33 KB (3,142 words) - 17:38, 21 February 2024
either spontaneously cyclize to form 1-pyrroline-5-carboxylic acid, which is reduced to proline by pyrroline-5-carboxylate reductase (using NADH or NADPH)...
23 KB (2,240 words) - 05:28, 11 November 2024
either spontaneously cyclize to form 1-pyrroline-5-carboxylic acid, which is reduced to proline by pyrroline-5-carboxylate reductase (using NADH or NADPH)...
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of IREDs. 3-Hydroxybutyrate dehydrogenase Opine dehydrogenase Pyrroline-2-carboxylate reductase Pyrroline-5-carboxylate reductase Mangas-Sanchez J, France...
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Biosynthesis (section Step 1: Initiation)
spontaneously cyclizes to pyrroline-5-carboxylate. Pyrroline-5-carboxylate is further reduced by the enzyme pyrroline-5-carboxylate reductase (P5CR) to yield...
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Pyrroline-5-carboxylate reductase 1, mitochondrial is an enzyme that in humans is encoded by the PYCR1 gene. This gene encodes an enzyme that catalyzes...
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giving off 33.5 kJ/mol of energy. The oxidative conversion of pyruvate into acetyl-CoA is referred to as the pyruvate dehydrogenase reaction. It is...
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L-malate, catalyzed by malate dehydrogenase, in the citric acid cycle. Malate is also oxidized by succinate dehydrogenase in a slow reaction with the initial...
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K (2005). "Crystal structures of Delta1-piperideine-2-carboxylate/Delta1-pyrroline-2-carboxylate reductase belonging to a new family of NAD(P)H-dependent...
79 KB (9,020 words) - 21:04, 28 October 2024
Cutis laxa (redirect from Cutis laxa, recessive type 1)
Inheritance in Man (OMIM): Fibulin 5; FBLN5 - 604580 Online Mendelian Inheritance in Man (OMIM): Pyrroline-5-Carboxylate Reductase 1; PYCR1 - 179035 Online Mendelian...
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conjugate base and carboxylate is 2-oxoadipate or α-ketoadipate, which is the biochemically relevant form. Homoisocitrate dehydrogenase 2-oxoadipate - Compound...
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chromosome 14, at 14q24.3. NOXRED1 is predicted to be involved in pyrroline-5-carboxylate reductase activity as part of the L-proline biosynthetic pathway...
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The change in protonation state occurs at pH 4.07. This form with both carboxylates lacking protons is dominant in the physiological pH range (7.35–7.45)...
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List of EC numbers (EC 3) (redirect from EC 3.5)
deaminase EC 3.5.4.19: phosphoribosyl-AMP cyclohydrolase EC 3.5.4.20: pyrithiamine deaminase EC 3.5.4.21: creatinine deaminase EC 3.5.4.22: 1-pyrroline-4-hydroxy-2-carboxylate...
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cycle, where it is synthesized from α-ketoglutarate by α-ketoglutarate dehydrogenase through decarboxylation. During the process, coenzyme A is added. With...
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also known as 4-methyl-2-oxovaleric acid, and its conjugate base and carboxylate, α-ketoisocaproate, are metabolic intermediates in the metabolic pathway...
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oxidase MeSH D08.811.682.662.693 – 1-pyrroline-5-carboxylate dehydrogenase MeSH D08.811.682.662.695 – pyrroline carboxylate reductases MeSH D08.811.682.662...
158 KB (15,232 words) - 06:41, 8 March 2024
reacts with many reagents. These can be classified into N-centered and carboxylate-center reactions. Glycine is not essential to the human diet, as it is...
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3-Phosphoglyceric acid (category Carboxylate anions)
glycolysis) and the subsequent catalysis by glyceraldehyde 3-phosphate dehydrogenase into G3P. G3P eventually reacts to form the sugars such as glucose or...
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oxidation into agmatine-aldehyde, which is in turn converted by aldehyde dehydrogenase into guanidinobutyrate and secreted by the kidneys. Agmatine was found...
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81 (5): 2165–2178. doi:10.1128/JVI.02287-06. PMC 1865933. PMID 17166910. Goodier JL, Zhang L, Vetter MR, Kazazian HH (September 2007). "LINE-1 ORF1 protein...
183 KB (12,460 words) - 13:46, 23 September 2024