• Thumbnail for Branched-chain amino acid
    A branched-chain amino acid (BCAA) is an amino acid having an aliphatic side-chain with a branch (a central carbon atom bound to three or more carbon atoms)...
    29 KB (3,420 words) - 20:54, 29 August 2024
  • Thumbnail for Branched-chain amino acid aminotransferase
    Branched-chain amino acid aminotransferase (BCAT), also known as branched-chain amino acid transaminase, is an aminotransferase enzyme (EC 2.6.1.42) which...
    30 KB (3,560 words) - 09:51, 9 April 2024
  • like other branched-chain amino acids, is synthesized by bacteria and plants, but not by animals. It is therefore an essential amino acid in animals,...
    14 KB (1,188 words) - 12:26, 29 October 2024
  • Thumbnail for Leucine
    property it shares with many other amino acids. Like valine and isoleucine, leucine is a branched-chain amino acid. The primary metabolic end products...
    27 KB (4,132 words) - 00:11, 7 September 2024
  • BCKDC catalyzes an irreversible step in the catabolism of the branched-chain amino acids L-isoleucine, L-valine, and L-leucine, acting on their deaminated...
    16 KB (1,781 words) - 18:08, 24 April 2024
  • Thumbnail for Maple syrup urine disease
    affects the body's ability to metabolize amino acids due to a deficiency in the activity of the branched-chain alpha-ketoacid dehydrogenase (BCKAD) complex...
    45 KB (5,497 words) - 23:17, 8 November 2024
  • Thumbnail for Isoleucine
    Isoleucine (category Branched-chain amino acids)
    physiological pH), branched-chain, aliphatic amino acid. It is essential in humans, meaning the body cannot synthesize it. Essential amino acids are necessary...
    15 KB (1,404 words) - 19:31, 15 November 2024
  • Thumbnail for Α-Ketoisocaproic acid
    amino acid, and its degradation is critical for many biological duties. α-KIC is produced in one of the first steps of the pathway by branched-chain amino...
    12 KB (1,573 words) - 20:04, 31 October 2024
  • Thumbnail for Branched chain amino acid transaminase 1
    Branched chain amino acid transaminase 1 is a protein that in humans is encoded by the BCAT1 gene. It is the first enzyme in the branched-chain amino...
    8 KB (891 words) - 02:33, 6 September 2023
  • Thumbnail for Aromatic amino acid
    An aromatic amino acid is an amino acid that includes an aromatic ring. Among the 20 standard amino acids, histidine, phenylalanine, tryptophan, tyrosine...
    11 KB (1,066 words) - 00:48, 10 September 2024
  • called Branched Chain Amino Acid Exporters (LIV-E) mediate the export of branched chain amino acids out of prokaryotic cells. Branched chain amino acids (BCAAs)...
    11 KB (1,286 words) - 17:35, 10 June 2024
  • biochemical processes responsible for the synthesis of proteins and amino acids (anabolism), and the breakdown of proteins by catabolism. The steps of...
    27 KB (2,828 words) - 23:11, 3 November 2024
  • Thumbnail for Branched-chain keto acid dehydrogenase kinase deficiency
    have low levels of branched chain amino acids (BCAA) in their organism due to accelerated breakdown of these essential amino acids. This results in delayed...
    7 KB (711 words) - 15:02, 10 November 2024
  • barrier. The transport mechanism for tryptophan is shared with the branched chain amino acids (BCAAs), leucine, isoleucine, and valine. During extended exercise...
    29 KB (3,798 words) - 19:03, 21 June 2024
  • Thumbnail for Acetolactate synthase
    micro-organisms. ALS catalyzes the first step in the synthesis of the branched-chain amino acids (valine, leucine, and isoleucine). A human protein of yet unknown...
    18 KB (1,966 words) - 01:21, 12 September 2024
  • The branched chain amino acid:cation symporter (LIVCS) family (TC# 2.A.26) is a member of the APC superfamily. Characterized members of this family transport...
    3 KB (327 words) - 12:10, 23 September 2019
  • Thumbnail for Thiamine pyrophosphate
    ethanol fermentation Alpha-ketoglutarate dehydrogenase complex Branched-chain amino acid dehydrogenase complex 2-hydroxyphytanoyl-CoA lyase Transketolase...
    9 KB (868 words) - 17:30, 18 July 2024
  • Hydroxy/Aromatic Amino Acid Permease (HAAAP) Family TC# 2.A.78 - Branched Chain Amino Acid Exporter (LIV-E) Family TC# 2.A.95 - 6TMS Neutral Amino Acid Transporter...
    8 KB (726 words) - 06:56, 31 May 2024
  • Thumbnail for BCKDK
    BCKD behavior. Exceedingly high BCKD complex activity increases branched-chain amino acid catabolism and protein degradation in skeletal muscle, which is...
    13 KB (1,614 words) - 19:45, 6 November 2024
  • Thumbnail for 2-Aminoisobutyric acid
    2-Aminoisobutyric acid (also known as α-aminoisobutyric acid, AIB, α-methylalanine, or 2-methylalanine) is the non-proteinogenic amino acid with the structural...
    6 KB (454 words) - 11:49, 18 September 2023
  • Thumbnail for Alloisoleucine
    Alloisoleucine (category Branched-chain amino acids)
    classified as a branched-chain amino acid (BCAA). It is the rarest of the four. L-Alloisoleucine is a diastereomer of the proteogenic amino acid L-isoleucine...
    3 KB (202 words) - 00:23, 1 April 2024
  • involved in fatty acid β-oxidation (SCAD, MCAD, LCAD, VLCAD, and VLCAD2), and the other four are involved in branched chain amino acid metabolism (i3VD...
    17 KB (2,174 words) - 19:59, 29 August 2024
  • high-intensity exercise by increasing the muscle carnosine concentration. Branched-chain amino acids, leucine, isoleucine and valine are commonly used for their muscle...
    48 KB (5,480 words) - 05:22, 5 November 2024
  • Thumbnail for Tryptophan
    an α-amino acid that is used in the biosynthesis of proteins. Tryptophan contains an α-amino group, an α-carboxylic acid group, and a side chain indole...
    52 KB (5,315 words) - 22:39, 7 October 2024
  • branched-chain fatty acid synthesis. The activity of this enzyme is much higher with branched-chain α-keto acid substrates than with straight-chain substrates...
    41 KB (4,751 words) - 20:26, 4 September 2024
  • Thumbnail for Β-Hydroxy β-methylbutyric acid
    synthesized in the human body through the metabolism of L-leucine, a branched-chain amino acid. In healthy individuals, approximately 60% of dietary L-leucine...
    106 KB (9,982 words) - 15:37, 7 January 2024
  • Thumbnail for Isovaleric acidemia
    disorder which disrupts or prevents normal metabolism of the branched-chain amino acid leucine. It is a classical type of organic acidemia. A characteristic...
    9 KB (839 words) - 16:17, 28 October 2024
  • Thumbnail for Citric acid cycle
    aerobic respiration. In addition, the cycle provides precursors of certain amino acids, as well as the reducing agent NADH, that are used in numerous other...
    56 KB (6,064 words) - 00:44, 9 November 2024
  • Thumbnail for 2-Hydroxyisocaproic acid
    2-Hydroxyisocaproic acid (HICA or leucic acid) is a metabolite of the branched-chain amino acid leucine. It is commonly sold as a purported muscle building...
    4 KB (293 words) - 06:57, 17 August 2021
  • complete amino acid profiles of various proteins. *Semi-essential, under certain conditions **Branched-chain amino acid (BCAA) While the amino acid scores...
    33 KB (1,799 words) - 01:22, 25 October 2024