Short-chain acyl-CoA dehydrogenase (EC 1.3.8.1, butyryl-CoA dehydrogenase, butanoyl-CoA dehydrogenase, butyryl dehydrogenase, unsaturated acyl-CoA reductase...
4 KB (431 words) - 03:14, 30 March 2024
levels of short-chain acyl-CoA dehydrogenase, which is important for breaking down short-chain fatty acids. Low levels of this enzyme halt short-chain fatty...
9 KB (709 words) - 22:51, 29 April 2024
ACADS (redirect from Short-chain acyl-coenzyme A dehydrogenase)
Acyl-CoA dehydrogenase, C-2 to C-3 short chain is an enzyme that in humans is encoded by the ACADS gene. This gene encodes a tetrameric mitochondrial flavoprotein...
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specificity for short-, medium-, or long-chain fatty acid acyl-CoA substrates. While different dehydrogenases target fatty acids of varying chain length, all...
17 KB (2,171 words) - 21:48, 4 August 2024
Medium-chain acyl-CoA dehydrogenase deficiency (MCAD deficiency or MCADD) is a disorder of fatty acid oxidation that impairs the body's ability to break...
15 KB (1,670 words) - 22:40, 29 December 2023
long-chain-acyl-dehydrogenase) deficiency is exclusively linked to genetic mutations in DNA. A change of the gene that codes for very long-chain-acyl-CoA-dehydrogenase...
10 KB (1,061 words) - 09:28, 26 July 2023
Acyl-CoA is a group of coenzymes that metabolize carboxylic acids. Fatty acyl-CoA's are susceptible to beta oxidation, forming, ultimately, acetyl-CoA...
11 KB (1,195 words) - 19:28, 5 June 2024
Long-chain acyl-CoA dehydrogenase (EC 1.3.8.8, palmitoyl-CoA dehydrogenase, palmitoyl-coenzyme A dehydrogenase, long-chain acyl-coenzyme A dehydrogenase,...
4 KB (403 words) - 14:47, 26 August 2023
Medium-chain acyl-CoA dehydrogenase (EC 1.3.8.7, fatty acyl coenzyme A dehydrogenase (ambiguous), acyl coenzyme A dehydrogenase (ambiguous), acyl dehydrogenase...
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List of causes of hypoglycemia (category Articles with short description)
disease Mcquarrie type infantile idiopathic hypoglycemia Medium chain acyl-CoA dehydrogenase deficiency Mesothelioma Methylmalonic acidemia Mitiglinide Mitochondrial...
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Beta oxidation (category Articles with short description)
long chain fatty acids are oxidized in peroxisomes. The overall reaction for one cycle of beta oxidation is: Cn-acyl-CoA + FAD + NAD+ + H2O + CoA → Cn-2-acyl-CoA...
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long-chain 3-hydroxyacyl-coenzyme A (CoA) dehydrogenase, which is part of a protein complex known as mitochondrial trifunctional protein. Long-chain fatty...
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decarboxylation of branched, short-chain alpha-ketoacids. BCKDC is a member of the mitochondrial α-ketoacid dehydrogenase complex family, which also includes...
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ACADSB (category Articles with short description)
short/branched chain specific acyl-CoA dehydrogenase (SBCAD), an enzyme in the acyl CoA dehydrogenase family. It can cause short/branched-chain acyl-CoA...
8 KB (1,142 words) - 00:40, 6 March 2022
Pyruvate dehydrogenase complex (PDC) is a complex of three enzymes that converts pyruvate into acetyl-CoA by a process called pyruvate decarboxylation...
29 KB (3,340 words) - 12:35, 25 July 2024
Scad (category Short description is different from Wikidata)
colitis associated with diverticulosis, a type of colitis Short-chain acyl-CoA dehydrogenase, an enzyme Scad, name for various fish in the jack family...
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namely acyl-CoA dehydrogenase, enoyl-CoA hydratase, 3-hydroxyacyl-CoA dehydrogenase, and thiolase. The cycle produces a new fatty acid chain with two...
22 KB (2,106 words) - 23:15, 5 August 2024
causes branched-chain keto acid dehydrogenase kinase deficiency. The BCKDH complex converts branched-chain amino acids into acyl-CoA derivatives, which...
29 KB (3,420 words) - 14:14, 26 May 2024
Methylene cyclopropyl acetic acid (category Articles with short description)
a number of Acyl-CoA dehydrogenases. The inhibition of one in particular, butyryl CoA dehydrogenase (a short-chain acyl-CoA dehydrogenase), causes β-oxidation...
7 KB (672 words) - 13:01, 24 February 2024
unsaturated acyl coenzyme A reductase, butyryl coenzyme A dehydrogenase, short-chain acyl CoA dehydrogenase, short-chain acyl-coenzyme A dehydrogenase, 3-hydroxyacyl...
2 KB (165 words) - 13:37, 26 August 2023
Type 2 diabetes (category Articles with short description)
caused by a misfolding variant of the mitochondrial protein short-chain acyl-CoA dehydrogenase". Journal of Inherited Metabolic Disease. 34 (2): 465–475...
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Glutaric acidemia type 2 (redirect from Multiple acyl-CoA dehydrogenase deficiency)
ISSN 1879-0038. PMC 7949704. PMID 33450351. "#231680 - MULTIPLE ACYL-CoA DEHYDROGENASE DEFICIENCY; MADD". www.omim.org. Retrieved 2023-12-06. "Glutaric...
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List of diseases (S) (category Articles with short description)
Shock Shokeir syndrome Short bowel syndrome Short broad great toe macrocranium Short-chain acyl-CoA dehydrogenase deficiency Short limb dwarf lethal Colavita–Kozlowski...
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Glutaryl-CoA dehydrogenase (GCDH) is an enzyme encoded by the GCDH gene on chromosome 19. The protein belongs to the acyl-CoA dehydrogenase family (ACD)...
6 KB (836 words) - 01:17, 7 March 2024
Astrocyte (category Articles with short description)
B.; Bross, P.; Gregersen, N. (June 2010). "Misfolding of short-chain acyl-CoA dehydrogenase leads to mitochondrial fission and oxidative stress". Molecular...
81 KB (9,291 words) - 11:24, 9 July 2024
ACADM (redirect from Medium-chain acyl-coenzyme A dehydrogenase)
ACADM (acyl-Coenzyme A dehydrogenase, C-4 to C-12 straight chain) is a gene that provides instructions for making an enzyme called acyl-coenzyme A dehydrogenase...
7 KB (955 words) - 09:28, 29 January 2023
In enzymology, an acyl-CoA dehydrogenase (NADP+) (EC 1.3.1.8) is an enzyme that catalyzes the chemical reaction acyl-CoA + NADP+ ⇌ {\displaystyle \rightleftharpoons...
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ACADVL (redirect from Very long-chain acyl-coenzyme A dehydrogenase)
Very long-chain specific acyl-CoA dehydrogenase, mitochondrial (VLCAD) is an enzyme that in humans is encoded by the ACADVL gene. Mutations in the ACADVL...
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2-Methylbutyryl-CoA dehydrogenase deficiency is an autosomal recessive metabolic disorder. It causes the body to be unable to process the amino acid isoleucine...
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Fatty acid (redirect from Long chain fatty acid)
"Medium-Chain Acyl-CoA Dehydrogenase Deficiency". Medscape. Beermann, C.; Jelinek, J.; Reinecker, T.; Hauenschild, A.; Boehm, G.; Klör, H.-U. (2003). "Short term...
54 KB (4,978 words) - 14:13, 19 July 2024