4-alpha-glucan-branching enzyme, also known as brancher enzyme or glycogen-branching enzyme is an enzyme that in humans is encoded by the GBE1 gene. Glycogen branching...

Glycogen-branching enzyme deficiency (GBED) is an inheritable glycogen storage disease affecting American Quarter Horses and American Paint Horses. It...

which causes a defect in the glycogen branching enzyme. Therefore, glycogen is not made properly and abnormal glycogen molecules accumulate in cells;...

the interior of the glycogen molecule. The branching enzyme can act upon only a branch having at least 11 residues, and the enzyme may transfer to the...

non-reducing end of the glycogen chain, forming more α(1→4) bonds in the process. Branches are made by glycogen branching enzyme (also known as...

Valberg, Stephanie; James R Mickelson. "Glycogen Branching Enzyme Deficiency (GBED) in Horses". Glycogen Branching Enzyme Deficiency (GBED). University of Minnsesota...

glycogen-branching enzyme deficiency. This condition is caused by a mutation of the GBE1 gene responsible for producing the glycogen branching enzyme...

breed's Glycogen branching enzyme (GBE1) can cause both a perinatal hypoglycemic collapse and a late-juvenile-onset neuromuscular degeneration in glycogen storage...

A glycogen storage disease (GSD, also glycogenosis and dextrinosis) is a metabolic disorder caused by a deficiency of an enzyme or transport protein affecting...

The glycogen debranching enzyme, in humans, is the protein encoded by the gene AGL. This enzyme is essential for the breakdown of glycogen, which serves...

sequential removal of glucose monomers via phosphorolysis, by the enzyme glycogen phosphorylase. In the muscles, glycogenolysis begins due to the binding...

carbohydrates metabolism. Glycogen storage diseases are deficiencies of enzymes or transport proteins which impair glycogen synthesis, glycogen degradation or glycolysis...

for glycogen branching enzyme, also called 1,4-alpha-glucan-branching enzyme. The GBE1 gene provides instructions for making the glycogen branching enzyme...

Glycogen phosphorylase is one of the phosphorylase enzymes (EC 2.4.1.1). Glycogen phosphorylase catalyzes the rate-limiting step in glycogenolysis in...

control Genome Biology and Evolution, a scientific journal Glycogen branching enzyme, an enzyme The general balance equation, a simplified mass balance relation...

produced after hydrolysis of glycogen. Without glycogen debranching enzymes to further convert these branched glycogen polymers to glucose, limit dextrinosis...

breakdown of glycogen to glucose-1-phosphate for use in muscle. The enzyme removes 1,4 glycosyl residues from outer branches of glycogen and adds inorganic...

Quarter Horses and Appaloosas), malignant hyperthermia (MH) and glycogen branching enzyme deficiency (GBED). The influence of Thoroughbred breeding puts...

intermediate and highly branched maltodextrins produced from gelatinized starches with various microbial glycogen branching enzymes". Carbohydrate Polymers...

extensively branched and compact than starch. Glycogen is a polymer of α(1→4) glycosidic bonds linked with α(1→6)-linked branches. Glycogen is found in...

an enzyme involved in converting glucose to glycogen. It acts as a primer, by polymerizing the first few glucose molecules, after which other enzymes take...

Isoamylase (EC 3.2.1.68, debranching enzyme, glycogen α-1,6-glucanohydrolase) is an enzyme with systematic name glycogen 6-α-D-glucanohydrolase. It catalyses...

core protein Glycogenin, surrounded by branches of glucose units, linked together. The branching of glycogen increases its solubility, and allows for...

extract different glycolytic enzymes from muscle tissue, and combine them to artificially create the pathway from glycogen to lactic acid. In one paper...

up") Equine polysaccharide storage myopathy (EPSM) or (PSSM) Glycogen Branching Enzyme Deficiency (GBED) Hypocalcemia Hyperkalemic periodic paralysis...

the branching enzyme in mycobacteria makes shorter branches compared to glycogen synthesis. For organisms that can utilize both classic glycogen synthesis...

maltase enzymes, providing two glucose molecules that can be further processed: either broken down to provide energy, or stored as glycogen. The lack...

of an α-linked glucose polymer with a degree of branching intermediate between amylopectin and glycogen, though more similar to the former. The polymers...

production of hormones, conversion and storage of nutrients such as glucose and glycogen, and the decomposition of red blood cells. The liver is also an accessory...

and the branched amylopectin. Depending on the plant, starch generally contains 20 to 25% amylose and 75 to 80% amylopectin by weight. Glycogen, the energy...