person with a fatty-acid metabolism disorder will still send fats to the liver. The fats are broken down to fatty acids. The fatty acids are then transported...
9 KB (971 words) - 14:49, 10 October 2024
Fatty acid metabolism consists of various metabolic processes involving or closely related to fatty acids, a family of molecules classified within the...
50 KB (5,561 words) - 07:03, 13 August 2024
Beta oxidation (redirect from Fatty acid oxidation)
In biochemistry and metabolism, beta oxidation (also β-oxidation) is the catabolic process by which fatty acid molecules are broken down in the cytosol...
32 KB (3,381 words) - 18:51, 5 November 2024
Numerous genetic disorders are caused by errors in fatty acid metabolism. These disorders may be described as fatty oxidation disorders or as a lipid storage...
4 KB (356 words) - 19:39, 30 October 2024
cholesterol. Other types of lipids found in the body are fatty acids and membrane lipids. Lipid metabolism is often considered the digestion and absorption process...
23 KB (2,461 words) - 05:56, 15 October 2024
Omega−3 fatty acids, also called omega−3 oils, ω−3 fatty acids or n−3 fatty acids, are polyunsaturated fatty acids (PUFAs) characterized by the presence...
115 KB (12,761 words) - 02:00, 21 September 2024
Medium-chain triglyceride (redirect from Medium chain fatty acid)
Patients who have malnutrition, malabsorption or particular fatty-acid metabolism disorders are treated with MCTs because MCTs do not require energy for...
18 KB (1,877 words) - 05:24, 25 October 2024
acid (DHA) is an omega−3 fatty acid that is an important component of the human brain, cerebral cortex, skin, and retina. It is given the fatty acid notation...
30 KB (3,189 words) - 02:11, 21 September 2024
Adrenoleukodystrophy (category Fatty-acid metabolism disorders)
of fatty acid buildup caused by failure of peroxisomal fatty acid beta oxidation which results in the accumulation of very long chain fatty acids in tissues...
36 KB (3,703 words) - 17:24, 19 October 2024
Medium-chain acyl-coenzyme A dehydrogenase deficiency (category Fatty-acid metabolism disorders)
MCADD) is a disorder of fatty acid oxidation that impairs the body's ability to break down medium-chain fatty acids into acetyl-CoA. The disorder is characterized...
14 KB (1,670 words) - 15:38, 27 October 2024
Acyl-CoA (category Metabolism)
a fatty acid metabolism disorder. Acyl-CoA is important because this enzyme helps make Acyl-CoA from free fatty acids, and this activates the fatty acid...
11 KB (1,197 words) - 22:29, 7 November 2024
metabolism (organic acidurias) alkaptonuria Combined malonic and methylmalonic aciduria (CMAMMA) 2-hydroxyglutaric acidurias Disorders of fatty acid oxidation...
15 KB (1,526 words) - 15:07, 30 October 2024
Systemic primary carnitine deficiency (category Fatty-acid metabolism disorders)
Carnitine is an important amino acid for fatty acid metabolism. When carnitine cannot be transported into tissues, fatty acid oxidation is impaired, leading...
12 KB (1,279 words) - 20:39, 29 October 2024
Refsum disease (redirect from Phytanic acid storage disease)
plays physiologically in humans, but has been found to regulate fatty acid metabolism in the liver of mice. Individuals with Refsum disease present with...
13 KB (1,344 words) - 17:35, 28 September 2024
2013). "The role of short-chain fatty acids in the interplay between diet, gut microbiota, and host energy metabolism". Journal of Lipid Research. 54...
34 KB (3,252 words) - 16:04, 12 October 2024
Combined malonic and methylmalonic aciduria (category Fatty-acid metabolism disorders)
"The emerging role of the mitochondrial fatty-acid synthase (mtFASII) in the regulation of energy metabolism". Biochimica et Biophysica Acta (BBA) - Molecular...
31 KB (3,256 words) - 19:45, 30 October 2024
Very long-chain acyl-coenzyme A dehydrogenase deficiency (category Fatty-acid metabolism disorders)
Very long-chain acyl-coenzyme A dehydrogenase deficiency is a fatty-acid metabolism disorder which prevents the body from converting certain fats to energy...
10 KB (1,061 words) - 09:28, 26 July 2023
Alcohol Alcohol use disorder is one of the causes of fatty liver due to production of toxic metabolites like aldehydes during metabolism of alcohol in the...
38 KB (3,896 words) - 12:27, 19 October 2024
inhibitors Fatty acid synthesis Fatty acid metabolism Fatty acid degradation Enoyl-acyl carrier protein reductase List of fatty acid metabolism disorders Paiva...
35 KB (4,020 words) - 10:13, 27 March 2024
biochemistry, fatty acid synthesis is the creation of fatty acids from acetyl-CoA and NADPH through the action of enzymes called fatty acid synthases. This...
41 KB (4,751 words) - 20:26, 4 September 2024
humans. These effects occur through its metabolism by mitochondria to generate ATP during fatty acid metabolism or through one or more of its histone-modifying...
65 KB (6,431 words) - 13:44, 21 November 2024
immediate period after delivery. It is thought to be caused by a disordered metabolism of fatty acids by mitochondria in the fetus, caused by long-chain 3-hydroxyacyl-coenzyme...
17 KB (1,954 words) - 12:21, 20 October 2024
glucose and convert it into storage molecules such as fatty acids and glycogen. The metabolism of glycogen is controlled by activity of phosphorylase...
113 KB (12,407 words) - 11:21, 2 November 2024
odd-chain fatty acids (although not even-chain fatty acids, see below); and from other parts of metabolism they include lactate from the Cori cycle. Under...
20 KB (2,294 words) - 16:30, 29 June 2024
Carnitine (category Beta hydroxy acids)
involved in metabolism in most mammals, plants, and some bacteria. In support of energy metabolism, carnitine transports long-chain fatty acids from the...
33 KB (3,582 words) - 20:12, 9 November 2024
overlap with the symptoms of another metabolic myopathy, that of fatty acid metabolism disorders. DNA testing is helpful for determining between the similar...
43 KB (3,582 words) - 16:26, 16 October 2024
Carnitine palmitoyltransferase I deficiency (category Fatty-acid metabolism disorders)
deficiency is a rare metabolic disorder that prevents the body from converting certain fats called long-chain fatty acids(LCFA) into energy, particularly...
7 KB (599 words) - 15:56, 16 October 2024
Carnitine palmitoyltransferase II deficiency (category Fatty-acid metabolism disorders)
recessively inherited genetic metabolic disorder characterized by an enzymatic defect that prevents long-chain fatty acids from being transported into the mitochondria...
26 KB (3,163 words) - 15:55, 16 October 2024
Metabolic myopathy (category Inborn errors of metabolism)
of the muscle cell. Fatty acid metabolism disorder (fatty acid oxidation disorder, FAOD)—defect in fat (lipid) metabolism, anywhere along the pathway, starting...
51 KB (5,290 words) - 14:37, 30 October 2024
Vaccenic acid is a naturally occurring trans fatty acid and an omega-7 fatty acid. It is the predominant kind of trans-fatty acid found in human milk,...
12 KB (1,294 words) - 03:32, 18 September 2024