Propionyl-CoA carboxylase (EC 6.4.1.3, PCC) catalyses the carboxylation reaction of propionyl-CoA in the mitochondrial matrix. PCC has been classified...

both propionyl-CoA as well as acetyl-CoA. Propionyl-CoA is later converted into succinyl-CoA through biotin-dependant propionyl-CoA carboxylase (PCC)...

Propionic acidemia, also known as propionic aciduria or propionyl-CoA carboxylase deficiency (PCC deficiency), is a rare autosomal recessive metabolic...

Holocarboxylase synthetase (biotin—(propionyl-Coenzyme A-carboxylase (ATP-hydrolysing)) ligase)), also known as protein—biotin ligase, is a family of enzymes...

Propionyl coenzyme A carboxylase may refer to: Methylmalonyl-CoA decarboxylase, an enzyme Propionyl-CoA carboxylase, an enzyme This set index page lists...

3-methylcrotonyl CoA. The MCC holoenzyme is thought to be a heterododecamer (6α6β) with close structural analogy to propionyl-CoA carboxylase (PCC), another...

as intragenic complementation or interallelic complementation. Propionyl-CoA carboxylase (PCC) is a dodecameric heteropolymer composed of α and β subunits...

converted to Methylmalonyl-CoA by the enzyme propionyl-CoA Carboxylase. It then is converted into succinyl-CoA by methylmalonyl-CoA mutase (MUT). This reaction...

metabolism in CNS: expression pattern of methylmalonyl-CoA mutase and propionyl-CoA carboxylase alpha-subunit in developing and adult rat brain". Neuroscience...

mitochondria propionyl-CoA carboxylase with biotin as a cofactor to produce (S)-methylmalonyl-CoA. This is subsequently converted to (R)-methylmalonyl-CoA by mitochondrial...

succinyl-CoA through biotin-dependant propionyl-CoA carboxylase (PCC) and Vitamin B12-dependant methylmalonyl-CoA mutase (MCM), sequentially. Succinyl-CoA is...

hand, in Haloferax mediterranei, propionyl-CoA carboxylase, the BCCP pccA (I3R7G3) is fused with biotin carboxylase. The biosynthesis of fatty acids in...

Earth. Many carboxylases, including Acetyl-CoA carboxylase, Methylcrotonyl-CoA carboxylase, Propionyl-CoA carboxylase, and Pyruvate carboxylase require biotin...

first is propionyl-CoA carboxylase. This enzyme is responsible for carboxylating the α-carbon of a propionyl-CoA to produce D-methylmalonyl-CoA. After this...

(S)-methylmalonyl-CoA by the enzyme Propionyl-CoA carboxylase. Methylmalonyl CoA epimerase then catalyzes the rearrangement of (S)-methylmalonyl-CoA to the (R)...

a biotin co-factor, ATP and the enzyme propionyl-CoA carboxylase. The bicarbonate ion's carbon is added to the middle carbon of propionyl-CoA, forming...

(S)-methylmalonyl-CoA carboxy-lyase (propanoyl-CoA-forming). Other names in common use include propionyl-CoA carboxylase, propionyl coenzyme A carboxylase, methylmalonyl-coenzyme...

syndrome Pramlintide Pregnancy Premature labour and/or delivery Propionyl-CoA carboxylase deficiency PCCA type Pyloroplasty Quinine Reactive hypoglycemia...

complex concentrate, a medication Propionyl-CoA carboxylase, catalyses the carboxylation reaction of propionyl CoA in the mitochondrial matrix...

metabolism in CNS: expression pattern of methylmalonyl-CoA mutase and propionyl-CoA carboxylase alpha-subunit in developing and adult rat brain". Neuroscience...

propionyl-CoA, is converted into D-methylmalonyl-CoA by propionyl-CoA carboxylase and then converted into L-methylmalonyl-CoA by methylmalonyl-CoA epimerase...

propionylation is propionyl-CoA. Propionyl-CoA in the cell is metabolised by the enzyme propionyl-CoA carboxylase. Accumulation of propionyl-CoA leads to increased...

acetyl-CoA out of the mitochondrion). This cytosolic acetyl-CoA can then be used to synthesize fatty acids through carboxylation by acetyl-CoA carboxylase into...

carboxylase (MCC) Propionyl-CoA carboxylase (PCC) For the first two, biotin serves as a cofactor responsible for transfer of bicarbonate to acetyl-CoA, converting...

five carboxylases in the human body (propionyl-CoA carboxylase, methylcrotonyl-CoA carboxylase, pyruvate carboxylase, and 2 forms of acetyl-CoA carboxylase...

the intragenic complementation in the heteromultimeric protein propionyl-CoA carboxylase". Biochimica et Biophysica Acta (BBA) - Molecular Basis of Disease...

biochemical reactants help support life. Tetrahydrofolate is a necessary co-reactant for synthesizing some amino acids, such as glycine. Heme B is the...

the intragenic complementation in the heteromultimeric protein propionyl-CoA carboxylase. Biochim Biophys Acta. 2005;1740(3):489-498. doi:10.1016/j.bbadis...

Acetyl-CoA carboxylase catalyzes the carboxylation of the Acetyl-CoA to Malonyl-CoA and Propionyl-CoA carboxylase catalyses the carboxylation of propionyl-CoA...

acetyl-CoA carboxylase and propionyl-CoA carboxylase. These enzymes generate malonyl-CoA and (S)-methylmalonyl-CoA, respectively. Malonyl-CoA, in a series...