Carnitine is a quaternary ammonium compound involved in metabolism in most mammals, plants, and some bacteria. In support of energy metabolism, carnitine...
30 KB (3,278 words) - 20:35, 26 April 2024
Acetylcarnitine (redirect from Acetyl-L-carnitine)
Acetyl-L-carnitine, ALCAR or ALC, is an acetylated form of L-carnitine. It is naturally produced by the human body, and it is available as a dietary supplement...
16 KB (1,833 words) - 03:43, 18 September 2024
Carnitine palmitoyltransferase I (CPT1) also known as carnitine acyltransferase I, CPTI, CAT1, CoA:carnitine acyl transferase (CCAT), or palmitoylCoA transferase...
19 KB (2,464 words) - 00:31, 12 June 2024
Carnitine palmitoyltransferase II deficiency, sometimes shortened to CPT-II or CPT2, is an autosomal recessively inherited genetic metabolic disorder...
26 KB (3,163 words) - 15:55, 16 October 2024
primary carnitine deficiency (SPCD) is an inborn error of fatty acid transport caused by a defect in the transporter responsible for moving carnitine across...
12 KB (1,279 words) - 09:22, 11 April 2023
Carnitine palmitoyltransferase I deficiency is a rare metabolic disorder that prevents the body from converting certain fats called long-chain fatty acids(LCFA)...
7 KB (599 words) - 15:56, 16 October 2024
Carnitine O-acetyltransferase also called carnitine acetyltransferase (CRAT, or CAT) (EC 2.3.1.7) is an enzyme that encoded by the CRAT gene that catalyzes...
14 KB (1,691 words) - 09:21, 3 June 2024
Carnitine O-palmitoyltransferase (also called carnitine palmitoyltransferase) is a mitochondrial transferase enzyme (EC 2.3.1.21) involved in the metabolism...
2 KB (151 words) - 07:15, 20 October 2022
Carnitine biosynthesis is a method for the endogenous production of L-carnitine, a molecule that is essential for energy metabolism. In humans and many...
14 KB (1,458 words) - 20:09, 4 September 2024
Carnitine-acylcarnitine translocase deficiency is a rare, autosomal recessive metabolic disorder that prevents the body from converting long-chain fatty...
5 KB (398 words) - 15:34, 16 October 2024
Carnitine O-palmitoyltransferase 2, mitochondrial is an enzyme that in humans is encoded by the CPT2 gene. Carnitine palmitoyltransferase II precursor...
9 KB (1,043 words) - 04:58, 4 July 2024
Glycine propionyl-L-carnitine (GPLC) is a propionyl ester of carnitine that includes an additional glycine component. Due to tissues esterases enzymes...
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membranes. Acyl-carnitine is shuttled inside by a carnitine-acylcarnitine translocase, as a carnitine is shuttled outside. Acyl-carnitine is converted back...
32 KB (3,377 words) - 04:07, 4 September 2024
Carnitine-acylcarnitine translocase (CACT) is responsible for passive transport of carnitine and carnitine-fatty acid complexes and across the inner mitochondrial...
2 KB (253 words) - 19:58, 29 August 2024
Carnitine O-octanoyltransferase (CROT or COT) is a member of the transferase family, more specifically a carnitine acyltransferase, a type of enzyme which...
12 KB (1,421 words) - 14:29, 22 September 2024
In enzymology, a carnitine 3-dehydrogenase (EC 1.1.1.108) is an enzyme that catalyzes the chemical reaction carnitine + NAD+ ⇌ {\displaystyle \rightleftharpoons...
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The enzyme carnitine decarboxylase (EC 4.1.1.42) catalyzes the chemical reaction carnitine ⇌ {\displaystyle \rightleftharpoons } 2-methylcholine + CO2...
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In enzymology, a carnitine dehydratase (EC 4.2.1.89) is an enzyme that catalyzes the chemical reaction L-carnitine ⇌ {\displaystyle \rightleftharpoons...
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Vitamin B4: can refer to the distinct chemicals choline, adenine, or carnitine. Choline is synthesized by the human body, but not sufficiently to maintain...
43 KB (2,802 words) - 14:46, 4 October 2024
movement. GA1 causes secondary carnitine deficiency, as glutaric acid, like other organic acids, is detoxified by carnitine. Mental retardation may occur...
26 KB (3,059 words) - 02:19, 14 October 2024
In enzymology, a (S)-carnitine 3-dehydrogenase (EC 1.1.1.254) is an enzyme that catalyzes the chemical reaction (S)-carnitine + NAD+ ⇌ {\displaystyle \rightleftharpoons...
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mitochondria oxidise considerable amounts of fat along with glucose. Carnitine transports long-chain fatty acids from the cytosol of the cell into the...
51 KB (4,002 words) - 02:10, 8 October 2024
carnitine deficiency - SLC22A5 (carnitine transporter) Carnitine-acylcarnitine translocase deficiency - Carnitine-acylcarnitine translocase Carnitine...
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several routes in nature. Well studied are the degradation of choline and carnitine. Trimethylamine is used in the synthesis of choline, tetramethylammonium...
17 KB (1,630 words) - 12:46, 2 September 2024
polypeptides, uptake of essential mineral nutrients, and in the production of carnitine, which is key in fatty acid metabolism. Lysine is also often involved...
68 KB (7,547 words) - 20:48, 20 October 2024
Ames, B. N. (2004). "Comparison of the effects of L-carnitine and acetyl-L-carnitine on carnitine levels, ambulatory activity, and oxidative stress biomarkers...
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of 3-hydroxyisovaleryl CoA does not occur (22). The transfer to carnitine by 4 carnitine acyl-CoA transferases distributed in subcellular compartments likely...
14 KB (1,416 words) - 10:31, 24 August 2024
substance, supplement or medicine that contains a TMA precursor (choline or carnitine) is ingested. Some precursor is absorbed into the bloodstream in the small...
34 KB (4,319 words) - 22:15, 10 September 2024
carnitine O-octanoyltransferase is an enzyme that in humans is encoded by the CROT gene. Carnitine octanoyltransferase (EC 2.3.1.137) is a carnitine acyltransferase...
4 KB (493 words) - 14:06, 13 October 2022
fatty-acid metabolism disorders. Carnitine Transport Defect Carnitine-acylcarnitine translocase deficiency (CACT) Carnitine Palmitoyl Transferase I & II (...
9 KB (971 words) - 14:49, 10 October 2024